Kronik idiopatik intestinal psödo-obstrüksiyona genellikle enterik sinir yada düz kasin hastaligi sebep olur ve rekürren intestinal obstrüksiyon ataklarina yol açar. Hastaligin klinik belirti ve bulgulari ile ya da rutin labarotuar incelemeleri ile ayirici tanisinin yapilmasi imkansizdir ve çogunlukla hastaya kesin tani konuluncaya kadar birkaç kere gereksiz laparatomi yapilmis olur. Kesin tani için tam kat barsak biyopsisi gereklidir. Burada; PAS boyasi ile dejenere olmus myofibrillerde, sitoplazmada inklüzyon cisimlerinin mikroskopik olarak tanimlanmasi ile tani konmus ve kronik idiopatik intestinal obstrüksiyon tanisi almis bir hasta, literatür siginda sunulmaktadir. Bu hasta altinci dekatta tani alan birkaç hastadan biridir.
Chronic idiopathic intestinal pseudo-obstruction is usually caused by disease of the enteric nerves or smooth muscle and results in recurrent episodes of intestinal obstruction. It is impossible to identify by clinical appearance and routine laboratory study, and there are a few reports of mostly unnecessary laparotomy. A full-thickness intestinal biopsy is necessary for a certain diagnosis. Here, a patient diagnosed microscopically (In periodic acid-Schiff [PAS] staining, PAS is positive and inclusions (PASx1000) consist of degenerated myofibrils) with chronic idiopathic intestinal pseudo-obstruction is presented in light of the available literature. Diagnosis of chronic idiopathic intestinal pseudo-obstruction in this patient was delayed until the sixth decade.