Hemofagositik sendrom; makrofajlarin kan hücrelerini fagosite etmesiyle karakterize ve ates, hepatosplenomegali, pansitopeni gibi bulgularla kendini gösteren klinik bir tablodur. Hemofagositik sendromun etyolojisinde baslica enfeksiyonlar, hematolojik maliniteler ve bag doku hastali klari yer almaktadir. Bu yazida hemofagositik sendrom ve fulminan hepatit birlikteligi gösteren bir olgu sunulmaktadir.
Hemophagocytic syndrome is a clinical manifestation of hemophagocytosis that is characterized by high fever, hepatosplenomegaly, and pancytopenia. Infections, hematological malignancies and connective tissue diseases are the main etiological factors of hemophagocytic syndrome. In this article, we present a case with fulminant hepatic failure associated with hemophagocytic syndrome.