Nadir görülen immünglobulin-E aracili olmayan bir gida asiri duyarliligi olan besin proteini ile iliskili enterokolit sendromu, asiri kusma,ishal ve akut dehidratasyon ile karakterizedir. Spesi?k bir laboratuvar bulgusu yoktur, ancak lökositoz, metabolik asidoz ve nadiren methemoglo- binemi görülebilir. Birincil tedavi, alerjik reaksiyona neden olan gidanin ortadan kaldirilmasini içerir. Burada methemoglobineminin eslik ettigi akut besin proteini ile iliskili enterokolit sendromu tanisi konulan 45 günlük bir kiz infant olgusu sunulmustur.
Food protein-induced enterocolitis syndrome, an uncommon non-immunoglobuline-E mediated food hypersensitivity, is charac-terized by profuse vomiting, diarrhea and acute dehydration. There are no speci?c laboratory ?ndings, however leukocytosis, metabolic acidosis and rarely methemoglobinemia may be observed. The primary treatment involves elimination of the food that causes the allergic reaction. Here we report the case of a 45-day-old female infant diagnosed acute food protein-induced enterocolitis syndrome co-existing with methemoglobinemia.