Primer biliyer siroz intrahepatik safra kanallarinda nonsüpüratif destrüksiyonla karakterize kronik, kolestatik, otoimmün bir karaciger hastalığıdir. Otoimmün hastalıklarla malignitelerin, özellikle de lenfoproliferatif hastalıkların birlikte görülebildigi bilinmektedir. Ancak primer biliyer siroz ve multipl myelom birlikteligi oldukça nadirdir. Bu yazida primer biliyer siroz ve multipl myelom beraberligi gösteren bir olgu sunulmuştur.
Primary biliary cirrhosis is a chronic, cholestatic, autoimmune liver disease characterized by nonsuppurative destruction of intrahepatic bile ducts. The association between autoimmune diseases and malignancy, especially lymphoproliferative disorders, has been well-defined. However, association of primary biliary cirrhosis and multiple myeloma is very rare. In this article, we present a case of primary biliary cirrhosis associated with multiple myeloma.